4 The possibility of amniotic bands is also ascribed.Ĭoncerning our patient as in most of the cases described in literature, it was a sporadic case and no familial recurrence has been reported. This thoracic type was explained embryonically by the rupture of the chorion at 3 weeks of gestation with resultant compression of the thoracic cavity and failure of descent of the heart at this stage. In the case described, the heart burst through a defect located on the anterior thoracic wall. Byron 3 classified ectopia cordis into four types: cervical, thoracic, thoracoabdominal and abdominal. This malformation is described as a partial or complete malposition of the heart outside the chest.
3 report that Haller was the first to use the term ectopia cordis to describe this malformation in 1706. 1 Ectopia cordis was first observed 5000 years ago. No autopsy was performed due to lack of parental consent.Įctopia cordis is a rare congenital abnormality. There were no other visible external malformations.
MAS TRANSPORTATION IN BYRON MI SKIN
It was not covered with a serous membrane or a skin ( Fig. The apex of the heart was oriented bottom and left ( Fig. The heart burst through this defect and was normal in appearance ( Fig. At the post-mortem examination at the Sylvanus Olympio University Hospital, there was a defect in the middle of the sternum. She died at her 22nd hour after birth, about 30 min before their arrival at the reference center. They attempt the referral hospital by public transport vehicle. The patient was referred after the neonatal cleansing and wrapping with a clean cloth. On clinical examination in birthroom, measurements were normal (Weight: 3000 g Height: 50 cm Cranial perimeter: 35 cm) there was no difficulty in breathing or cyanosis. The only obstetric ultrasound done at the 6th month did not detect any abnormality. The pregnancy was regularly followed up in prenatal consultations from the 2nd month. The mother also had no history of chronic ill health. There was no family history of any such or related congenital heart diseases She had no known exposure to teratogens. The father was 28 years old and the mother 27 years old.
She was the youngest of two children, the 07 years old brother having no visible malformation.
Case presentationĪ 10-hour-old, vaginally delivered full-term female neonate was referred from Bassar departmental hospital (400 km from Lome) to Sylvanus Olympio University Hospital (Lome) after finding a beating heart outside the thoracic cavity. It is the first case documented in a new born in our country. 4 We report a case of thoracic ectopia cordis, diagnosed in Bassar delivery room, in the north of Togo. 3 The thoracoabdominal type is generally associated with Cantrell's pentalogy or one of its variants including a bifid sternum, a diaphragmatic and anterior abdominal wall defect as well as an intracardiac malformation. 1,2 Four types have been described: cervical (5%), thoracic (65%), abdominal (10%) and thoraco-abdominal (20%). The estimated prevalence of ectopia cordis is 5–8 per million live births. Ectopia cordis is an extremely rare congenital cardiac malformation in which heart is partially or completely out of the thoracic cavity.
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